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The treatment is planed and developed for every unique patient, so that we can assure the best results for the patients and families.


NON SYNDROMIC CRANIOSYNOSTOSIS


Craniosynostosis may be defined as the premature closure or fusion of the calvarial sutures occurring in the uterus or shortly after birth. The calvarial sutures are lines of growth lying between the various bones of the skull. While there are a large number of sutures in the vault and base of the skull which can be involved, this discussion will be limited to the common ones on the top of the head.

These are six in number, namely the sagittal suture which runs longitudinally down the midline of the skull between the anterior and posterior fontanels, the metopic suture which runs longitudinally from the anterior fontanel to the area between the eyes, the two coronal sutures - one on each side running transversely from the anterior fontanel to the area just behind the orbits and the two lambdoid sutures which run obliquely downwards from the posterior fontanel to the areas behind the ears.

SYNDROMIC CRANIOSYNOSTOSIS


It includes the genetics craniosynostosis. The most frequent ones are: Crouzon Syndrome, Apert Syndrome, Pfeifer Syndrome among others.

Patients present a condition in which one or more of the fibrous sutures in an infant skull prematurely fuses. This results in restricted skull and brain growth. Because the brain cannot expand in the direction of the fused suture, it is forced to grow in the direction of the open sutures, often resulting in an abnormal head shape and facial features. Some cases of craniosynostosis may result in increased pressure on the brain and developmental delays. Craniotomy must be done before 1 year of age.

The most notable characteristic of Crouzon syndrome is cranial synostosis, but it usually presents as brachycephaly, which results in the appearance of a short and broad head. Exophthalmos (bulging eyes due to shallow eye sockets after arly fusion of surrounding bones), hypertelorism (greater than normal distance between the eyes), and psittichorhina (beak-like nose) are also symptoms.

Additionally, a common occurrence is external strabismus, which can be thought of as opposite from the eye position found in Down syndrome. Lastly, hypoplastic maxilla (insufficient growth of the midface) results in relative mandibular prognathism (chin appears to protrude despite normal growth of mandible) and gives the effect of the patient having a concave face.

Patients will need from 2 to 3 surgeries along their lives.

CROUZON SYNDROME

APERT SYNDROME

PFEIFER SYNDROME

SAETHRE-CHOTZEN SYNDROME

Hospital Sobrapar  •  2009 Av. Adolpho Lutz, 100 - Cidade Universitária - CP 6028 - 13083-880 - Campinas - SP - Brasil  •  Phone: +55 (19) 3749-9700
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